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Cardiovascular involvements in Behçet’s disease : «angio-Behçet»
Tridetti J. , Benoit A. , Borgoens P. , Hoffer E.
Rev Med Liege 2016, 71(1),22-27Abstract : Behçet’s disease is a relapsing, immune-mediated systemic vasculitis that may affect blood vessels of all types and sizes. Nowadays, the etiology remains unclear. In the absence of a biological marker or pathognomonic radiology, the diagnosis is mainly based on clinical manifestations. The cardiovascular involvement, known as «angio-Behçet», is relatively common and affects up to 40% of patients. It typically occurs in a young male, usually during the onset of the disease. In general, immunosuppressive and anticoagulant therapies initiated early are likely to induce a remarkable clinical improvement. Nevertheless, prompt recognition of the polymorphous cardiovascular manifestations of the disease is challenging and may be responsible for some considerable delay prior to initiation of adequate therapy. The aim of this article is to describe the spectrum of cardiovascular involvements of Behçet’s disease in order to optimize detection and therapeutic management.
